Kuumbwa kwemasero ose emuviri kunosanganisira esters e-fatty acid acids uye polyhydric alcohols. Izvi zvinokonzerwa nemakemikari anonzi phospholipids, ivo vane mutoro wekuchengetedza maitiro akajeka emishu, inobatanidzwa mumagadzirirwo emagetsi uye mumagetsi echolesterol. Ihwo hutano hwehutano hunoenderana nekuiswa kwezvinhu izvi.
AFS-syndrome - chii ichocho?
Anenge makore makumi matatu apfuura, rheumatologist Graham Hughes akawana chirwere umo maitiro epachiviriro anotanga kubudisa zvirwere zvakasimba zvinopesana ne phospholipid. Vanobatana pamaplatelet uye masvingo emasvingo, vanobatana nemapuroteni, kupinda mumagadzirirwo emagetsi uye kugadzirisa. Zvose zvechipiri uye yekutanga syndrome ye antiphospholipid antibodies ndiyo chirwere chekuzvimiririra chekusajekeswa kwakabva. Dambudziko iri rinowanzoita kuti vasikana vechidiki vave nemakore ekubereka.
Antiphospholipid syndrome - zvinokonzera
Kune rheumatologists asi zvakanga zvisingakwanisi kugadzirisa, nei kune kuonekwa sokurwara kana chirwere. Iko kune ruzivo runoti antiphospholipid syndrome inowanzotaridzirwa mune hama dzine chirwere chakafanana. Mukuwedzera kune hutano, nyanzvi dzinoti zvimwe zvimwe zvinhu zvinokonzera chirwere. Mumamiriro ezvinhu akadaro, AFS yechipiri inokura - izvo zvinokonzera kushandiswa kweanorifisi zvinosanganisira kufambira mberi kwezvimwe zvirwere zvine chokuita nekushanda kwemasimba ezvirwere. Nzira yekurapa inobva kune nzira dzekutanga kwechirwere.
Primary antiphospholipid syndrome
Urwu ruzhinji rwehutano hunozvimirira pachavo, uye kwete nechepamusoro pemamwe matambudziko mumuviri. Iyi syndrome ye antiphospholipid antibodies yakaoma kurapa nekuda kwekushaiwa kwekugumbura. Kazhinji chimiro chikuru chechirwere chacho chinenge chichiita sechinhu chisingaiti uye chinoratidzwa chave chiri mumatanho ekupedzisira ekufambira mberi kana kana zvichiitika zvinetso.
Secondary antiphospholipid syndrome
Izvi zvakasiyana-siyana zvinogadziriswa zvinokonzerwa nekuvapo kwemamwe zvirwere zvemuitiro kana zvimwe zviitiko zvechipatara. Kuvhiringidzika kwekutanga kwekudzivirira kwehutachiona hwezvirwere kunogona kutora mimba. Antiphospholipid syndrome muvakadzi vane pamuviri inowanikwa mu5% yemhosva. Kana chirwere ichi chiri mubvunzo chikaonekwa kare, kutakura kunowedzera zvakanyanya nzira yacho.
Zvirwere zvinonzi zvinokonzera antiphospholipid syndrome:
- hutachiona uye bhakitiriya;
- inocological neoplasms;
- nodular periarteritis;
- systemic lupus erythematosus.
Antiphospholipid syndrome - zviratidzo zvevakadzi
Chirwere chemakiriniki yehutachiona yakasiyana zvikuru uye isingaoneki, iyo inobatanidza kusiyana kwekutarisa. Dzimwe nguva chirwere chinowanikwa pasina zviratidzo, asi kazhinji antiphospholipid syndrome inoratidzika nenzira yechirwere chinowanzoitika chepamusoro uye midzi midzi yeropa (arteri kana mitsetse):
- pasi pamakumbo;
- chiropa;
- retina;
- ubongo;
- moyo;
- chiedza;
- itsvo.
Zviratidzo zvinozivikanwa zvevakadzi:
- chirevo chezvinyorwa pachiganda (chirevo chinonzi liveroid);
- myocardial infarction;
- migraines;
- kunonoka;
- kurwadziwa mubhokisi;
- varicose veins;
- thrombophlebitis;
- kurohwa;
- arterial hypertension;
- acute renal insufficiency;
- ascites;
- kuschemic ischemic ;
- kuoma kukuru kwakanyanya;
- necrosis yemapfupa uye zvinyoro zvinyoro;
- portal hypertension;
- utachipa kubuda ropa;
- chiropa chakakomba;
- spleen infarction;
- intrauterine fetal death;
- kuparadzaniswa kwepasipo.
Antiphospholipid syndrome - kuongororwa
Izvo zvakaoma kusimbisa kuvapo kwechirevo chinorondedzerwa chirwere, nokuti chinovhara kune dzimwe zvirwere, zvine zviratidzo zvisingaoneki. Kuti uongorore chirwere ichi, vanachiremba vanoshandisa mapoka maviri ekugadzirisa zviyero. Kuongororwa kwe antiphospholipid syndrome kunosanganisa kuunganidza an anamnesis. Rudzi rwekutanga rwezviratidzo zvekuongorora runosanganisira zvipatara zvinowanzoitika:
- Vascular thrombosis. Nhoroondo yezvokurapa inofanira kunge ine imwe kana kuti mamwe maitiro ekukuvadza kune mitsipa kana arteriya yakagadzirwa nechokushandisa uye laboratory.
- Dambudziko rekurwara. Mutsara uyu unofungidzirwa kana intrauterine fetal kufa yakaitika mushure mevhiki yegumi yekuberekwa kana kuberekwa kusati kwaitika kwakatarwa musati vhiki makumi matatu nemasere ekuberekwa musikana musipo kwechiromosomal, hormonal uye anatomical defect kubva kuvabereki.
Mushure mokunge nhoroondo yezvokurapa inounganidzwa, chiremba anogadza zvidzidzo zvakare. Antiphospholipid syndrome inopupurirwa apo pane kusanganiswa kwechirwere chekliniki uye chirongwa che laboratori (zvishoma). Mukufananidza, nhamba dzinoverengeka dzokusiyanisa zvirongwa zvinowanikwa. Nokuda kweizvi, nyanzvi inokurudzira kuti iwe uongorore mitsva inosabvisa zvirwere zvakafanana.
Antiphospholipid syndrome - kuongorora
Kuonekwa kwemaoreatori ezviratidzo zvechirwere chemazuva ano kunoshandiswa nekudzidza kwehupenyu hwehupenyu. Chiremba anogadza kuti ape ropa nokuda kwe antiphospholipid syndrome kuti aone kuvapo kwe plasma uye serum antibodies ku cardiolipins uye lupus anticoagulant. Uyezve, zvinotevera zvinogona kuonekwa:
- cryoglobulins;
- zvirwere zvekare kune erythrocytes;
- T- uye B-lymphocytes muwedzerwa kumira;
- antinuclear uye rheumatoid factor.
Dzimwe nguva chidzidzo chemazwi chinokurudzirwa chinobvumira kutsvaga zviratidzo zve antiphospholipid syndrome:
- HLA-DR7;
- HLA-B8;
- HLA-DR2;
- DR3-HLA.
Ko antipospholipid syndrome inorapwa sei?
Kurapa kwechirwere ichi chinotaridzika kunobva pane fomu (primary, secondary) uye kuoma kwezviratidzo zvechipatara. Zvinetso zvinomuka kana mukadzi ane pamuviri ane antiphospholipid syndrome - kurapwa kunofanira kusimbisa zviratidzo zvechirwere, kudzivirira hutachiona, uye zvakafanana hazviiti dambudziko kumucheche. Kuti zvive nekugadzirisa kusingaperi, rheumatologists vanoshandisa nzira yakabatana yekurapa.
Zvinoita here kuporesa antiphospholipid syndrome?
Kunyatsorambidza dambudziko rakatsanangurwa hazvibviri, kusvikira zvikonzero zvekuitika kwayo zvichisimbiswa. Antiphospholipid syndrome inoda kurapwa kwakakosha inotarisirwa kuderedza nhamba yezvirwere zvakakodzera muropa uye kudzivirira zvinetso zvepromboembolic. Mukufamba kwakanyanya kwechirwere, chirwere chinopesana nekuputika chinodiwa.
Kurapa kwe antiphospholipid syndrome - ikozvino mazano
Nzira huru yekubvisa zviratidzo zvehutano uku ndiko kushandiswa kwemaantiggregants uye anticoagulants zvechiito chisingaoneki:
- Acetylsalicylic acid (Aspirin uye zvakafanana);
- Warfarin ;
- Acenocoumarol;
- Phenylin;
- Dipyridamole.
Nzira yekurapa antiphospholipid syndrome - kliniki mazano:
- Rega kubva kusvuta, kunwa doro uye zvinodhaka, kunyora kwepurogiramu.
- Ruramisa kudya kwaidiwa nezvezvokudya zvakazara mu vitamini K - green tea, chiropa, mashizha mashizha miriwo.
- Kuzorora zvakakwana, tarisa hurumende yezuva racho.
Kana chirwere chemazuva ose chisina kubudirira, tsika yekurapa mimwe mishonga ndeyekuti:
- aminoquinolines - Plakvenil, Delagil;
- ruramisa anticoagulants - Clexan , Fraksiparin;
- glucocorticoids - Prednisolone , Methylprednisolone;
- inhibitors of platelet receptors - Tagren, Clopidogrel;
- heparinoids - Emeran, Sulodexide;
- cytostatics - Endoxane, Cytoxan;
- immunoglobulins (intravenous administration).
Mishonga yemagariro ne antiphospholipid syndrome
Hapana humwe hunobudirira humwe nzira dzokurapa, iyo chete inosarudzwa ndeyokutsvaga acetylsalicylic acid nemasikirwo ezvisikwa. Antiphospholipid syndrome haigoni kumira nekubatsira kwevanhu mapoka, nokuti anticoagulants yemasikirwo anewo unyoro. Usati washandisa nzira ipi zvayo yakakosha kunokosha kutarisa rheumatologist. Izvo chete nyanzvi inobatsira kuderedza antiphospholipid syndrome - zvirongwa zvechiremba zvinofanira kunyatsoongororwa.
Tea ine aspirin
Zvisungo:- Akaoma bark yemachena willow - 1-2 tsp.
- mvura inopisa - 180-220 ml.
Kugadzirira, shandisa :
- Miti yakasvibirira yakanyatsosuka uye geda.
- Brew willow inoputika nemvura inopisa, tsanidza maminitsi 20-25.
- Inwa mhinduro seyiyi katatu pazuva, unogona kutapira kuti unonaka.
Antiphospholipid syndrome - kufungidzira
Vese rheumatologist varwere vane izvo zvakaratidzwa kuongororwa zvinofanira kuonekwa kwenguva yakareba uye nguva dzose vanoita zvirongwa zvekudzivirira. Ndinogona kurarama kwenguva yakareba sei ne antiphospholipid syndrome, zvichienderana nemafomu ayo, kuoma uye kuvapo kwekugadzirisa zvirwere zvekudzivirira muviri. Kana chikamu chikuru cheAAPS chiine zviratidzo zvisinganzwisisiki chinoonekwa, kurapwa panguva yakakodzera uye kurapwa kwekudzivirira kunobatsira kudzivisa matambudziko, kufungidzira mumamiriro ezvinhu akadaro kunowanikwa zvakanaka.
Zvinhu zvinokuvadza ndezvekubatana kwechirwere ichi chiri mubvunzo ne lupus erythematosus, thrombocytopenia, inoramba iine arterial hypertension nezvimwe zvirwere. Mune mamiriro ezvinhu aya, kazhinji inoita antiphospholipid complex syndrome (yakaipa), iyo inoratidzwa nekuwedzera kwezviratidzo zvechipatara nekupora kwenguva refu. Mimwe migumisiro inogona kuguma kuuraya.
Antiphospholipid syndrome uye pamuviri
Iyo inorondedzerwa zvirwere ndeye chikonzero chinowanzokonzera kubvisa pamuviri, saka vanaamai vese vari mberi vachawana chirongwa cheprophylactic uye vopa ropa kune coagulogram. Antiphospholipid syndrome muvhiringidzika inonzi inonyanya kukonzera kufa kwekufa uye kupererwa, asi kuvapo kwayo hakusi kutonga. Mukadzi ane chirwere chakadaro anokwanisa kutakura uye kubereka mwana ane utano kana panguva yekuzvitakura iye achatevera mazano ose echiremba uye anotora antigregregants.
Izvo chirongwa chakafanana chinoshandiswa apo insemination yekugadzirira inorongwa. Antiphospholipid syndrome uye IVF zvakanyatsokwanisika, chete ndivo vachazofanira kushandisa zvinodhaka zvinodhaka. Kushandiswa kweanticoagulants uye antiggregants kuchaenderera mberi munguva yose yekuita gestation. Kubudirira kwehutano hwakadaro kwava pedyo ne100%.