Mhuka ine utano inodzivirirwa nemusununguko wemasero masero kubva kuhutachiona hwehutachiona, fungal uye bhakitiriya, allergens nezvimwe zvinhu zvisingafadzi. Primary immunodeficiency inorambidza munhu wechigadziro ichi kubva mumakore ekutanga ehupenyu, asi inogona kuratidzika pakukura. Ichi chirwere chinoda kugara ichiongororwa nenyanzvi uye kurapa kwenguva refu.
Kuenzanisa kwepakutanga kuberekwa kwemajeri
Ihwo hutano huri pasi pekufungidzirwa ndohwe marudzi mashanu, ayo anokonzerwa nokusakwanira:
1. Kusagadzikana kwemasero ekuchengetedzwa kwemasero:
- oroticide;
- chirwere cheDe Georgi;
- fermentopathy inotaridzika-biotin;
- kusakwana kwe purinucleoside phosphorylase.
2. Phagocytic primary immunodeficiency:
- chirwere chisingaperi chisinganyanyisi;
- cyclic uye chronic acyclic neutropenia;
- Miller's syndrome ("lazy leukocytes".
3. Kusakwanisa kwemasero emasanganisi:
- late immune start;
- Syndrome yaBruton;
- kusarudza kushayikwa kwezvirwere zvemunoglobulin.
4. Kusangana kwakakwana kwechiremera chemasero nechisimba:
- Wiskott-Aldrich syndrome;
- hypocalcemia ;
- reticular dysgenesis;
- Glanzmann-Riniker syndrome.
5. Kukundikana kwakakwana:
- Quincke-Osler's edema;
- lupus erythematosus;
- rheumatoid arthritis.
Zviratidzo zvepakutanga kusagadzikana
Izvo hazvina zviratidzo zvinogonesa kunyatsojekesa zvakatsanangurwa maitiro ezve genetic. Chipatara zviratidzo zvakasiyana kwazvo zvichienderana nemhando, chimiro uye kuoma kwechirwere chacho.
Kufungidzira kuti maitiro ekudzivirira immunodeficiency inobvira pane zviratidzo zvakadaro:
- kukanganisa kune dzimwe nguva zvirwere zvinotapukira uye zvirwere;
- izvo zvisinganyanyi kukosha zvekutora antibiotics;
- candidiasis yeganda nekudzokazve;
- epaccessed abscesses;
- pneumonia 2 uye dzimwe nguva gore;
- kugara otitis, sinusitis, bronchitis.
Kurapa kwepakutanga immunodeficiency
Utachiona hwakaoma, nokuti haugoni kuporesa chirwere. Kuvandudza mararamiro ehupenyu hwevarwere, kugara kwechirwere chisina kukodzera kubatwa nema immunoglobulins kunokosha, pamwe nekusarudza kusarura kwe antibacterial, antivirai uye antimycotic mazamu ezvirwere.
Radical therapy yeanorondedzwa chirwere inosanganisira mutema wemapfupa, izvo zviri nani kuitwa pazera duku. Asi zvakakosha kuziva kuti kushanda uku kunodhura zvikuru, uye dzimwe nguva zvakaoma kuwana mupi wehutano hwakakwana.