Primary immunodeficiency

Mhuka ine utano inodzivirirwa nemusununguko wemasero masero kubva kuhutachiona hwehutachiona, fungal uye bhakitiriya, allergens nezvimwe zvinhu zvisingafadzi. Primary immunodeficiency inorambidza munhu wechigadziro ichi kubva mumakore ekutanga ehupenyu, asi inogona kuratidzika pakukura. Ichi chirwere chinoda kugara ichiongororwa nenyanzvi uye kurapa kwenguva refu.

Kuenzanisa kwepakutanga kuberekwa kwemajeri

Ihwo hutano huri pasi pekufungidzirwa ndohwe marudzi mashanu, ayo anokonzerwa nokusakwanira:

1. Kusagadzikana kwemasero ekuchengetedzwa kwemasero:

2. Phagocytic primary immunodeficiency:

3. Kusakwanisa kwemasero emasanganisi:

4. Kusangana kwakakwana kwechiremera chemasero nechisimba:

5. Kukundikana kwakakwana:

Zviratidzo zvepakutanga kusagadzikana

Izvo hazvina zviratidzo zvinogonesa kunyatsojekesa zvakatsanangurwa maitiro ezve genetic. Chipatara zviratidzo zvakasiyana kwazvo zvichienderana nemhando, chimiro uye kuoma kwechirwere chacho.

Kufungidzira kuti maitiro ekudzivirira immunodeficiency inobvira pane zviratidzo zvakadaro:

Kurapa kwepakutanga immunodeficiency

Utachiona hwakaoma, nokuti haugoni kuporesa chirwere. Kuvandudza mararamiro ehupenyu hwevarwere, kugara kwechirwere chisina kukodzera kubatwa nema immunoglobulins kunokosha, pamwe nekusarudza kusarura kwe antibacterial, antivirai uye antimycotic mazamu ezvirwere.

Radical therapy yeanorondedzwa chirwere inosanganisira mutema wemapfupa, izvo zviri nani kuitwa pazera duku. Asi zvakakosha kuziva kuti kushanda uku kunodhura zvikuru, uye dzimwe nguva zvakaoma kuwana mupi wehutano hwakakwana.