Creutzfeldt-Jakob chirwere chirwere chisingawanzi chinokonzerwa nekuora kwehupi nekuda kwekuonekwa kwechinangwa chisinganzwisisiki cheprotein mu neurons uye chinonzi maasayendisiti avo vakatanga kutsanangura iyo. Chirwere chakanyanya kufanana pakati pevanhu vane makore 65 kusvika ku70.
Zvinokonzera Creutzfeldt-Jakob syndrome
Ive yakagadzirwa nesayenzi kuti chirwere cheCreutzzeldt-Jakob chirwere chinotapukira. Zvinonyatsozivikanwa kuti mumasero ehutano eropi uye mamwe maselo emuviri womunhu kune chirongwa chepakutanga chepuroteni, iro basa rayo rinoramba risinganzwisisi nhasi.
Chimwe chirwere chinotapukira chinotapukira, chinopinda mumuviri womunhu, chinopinda muuropi neropa, uko chinowedzera pane neurons. Uyezve, chirwere chechirwere chepachirwere, muhutano neprotini yakakwana yemasero europi, inokonzera shanduko muhutano hwayo, sechikonzero chekupedzisira zvishoma nezvishoma zvinoshanduka kuva pathogenic chimiro chakafanana nechinotapukisa prion. Abnormal prions form plaques uye zvinokonzera neuronal rufu.
Kurwara nepathogenic prions kunogona kuitika nenzira dzinotevera:
- apo kuiswa kwehutachiona hwehutachiona (ganda, cornea yeziso, ganda rakaoma reuropi);
- kuburikidza nechimwe chisina kukodzera sterilized neurosurgical instrument;
- uye kuwedzerwa ropa;
- pamwe nekuiswa kwemishonga yehomoni (gonadotropin yevanhu, somatotropin);
- apo paidya nyama yemhuka dzinorwara kana vanotakura utachiona (mombe, mbudzi, nezvimwewo).
Uyezve, chimwe chezvikonzero zvinokonzera chirwere ichocho chinokonzerwa nemararamiro anoenderana nekuchinja kwemajini. Zvimwe zviitiko zvechirwere zvine chinyorwa chisingazivikanwi.
Zviratidzo zveCreutzfeldt-Jakob chirwere
Chirwere cheCreutzfeldt-Jakob chine nguva yakareba yekudzikinura, iyo inosanganiswa nenguva iyo kupindira kwezvipembenene zvinotapukira muhutano tissue uye pathogenic kuchinja mumagariro ezvakanaka zvinoitika. Inguva yakareba sei izvi zvinopedzisira zvichitenderera pane nzira yehutachiona. Saka, kana hutachiwana hwehupi hutachiona hwehutachiona husina maturo, chirwere chacho chinowedzera mushure memwedzi gumi nemashanu, uye apo mishonga inotapukirwa inotangwa, mushure memakore gumi nemaviri.
Zvizhinji zveCreutzfeldt-Jakob chirwere chinowedzera kukura. Kune zvikamu zvitatu zvechirwere ichi, chinoratidzwa nezviratidzo zvakasiyana-siyana:
1. Nhanho yezviratidzo zvepodromal:
- kutsamwa;
- kuoma kuisa pfungwa;
- headaches ;
- chizoro;
- kushushikana kwehope;
- kuderera kwemaonero evanhu;
- kuchinja mumhinduro dzemitemo;
- kutya kwekutya kusina maturo;
- zviitiko zvisinganzwisisiki zvekufungidzira;
- kusagadzikana kwezvakaitwa;
- kukanganisa kuverenga mabasa, kuverenga.
2. Chikamu chekuratidzwa kwekliniki zviratidzo:
- kupera simba kwemuviri (kwemuzasi kana kumakumbo epamusoro, hafu yemuviri);
- chirwere chekubatana kwekuzvidira;
- kuora mwoyo kwakagumburwa ;
- musero rigidity;
- tremor, athetosis;
- myoclonus;
- dambudziko rekutaura;
- kushungurudzika kunetseka.
3. Terminal stage - inozivikanwa nehupamhi hwemodentia, umo varwere vari munharaunda yekufeva, vasingatauri. Pane musimba wakasimba musroti, hyperkinesia, kumedza zvinetso, zvinokonzera hyperthermia uye kugumburwa kweputi.
Kurapa uye kuguma kweCreutzfeldt-Jakob chirwere
Ichi chirwere mumatambudziko ose chinotungamirira kurufu. Hupenyu hunotarisirwa hwehuwandu hwevarwere hahupfuuri gore rimwe kubva panguva iyo kutanga kwechirwere ichi kutanga. Kusvika iye zvino, nzira dzekurapa chaiyo dziri mukushanda kunobudirira, uye varwere vanongorapwa chete.