Huntington's chorea chirwere chepachizvarwa chekuzvarwa, pamwe chete nekuratidzika kwekutenderera kusingabatsiri, kuderera kweuchenjeri uye kukura kwehutano hwepfungwa. Ichi chirwere chinogona kukura muvarume nevakadzi pane zvachose makore, asi kazhinji kacho zviratidzo zvekutanga zveHuntington's chorea zvinoratidzika mumazera emakore makumi matatu nemakumi matatu nemakumi mashanu.
Zviratidzo zveHonda hwaHuntington
Chiratidzo chekliniki chikuru chechirwere chaHuntington chiri chorea, iyo inoratidzirwa nekusavhiringidzika uye kutadza kusadzora. Pakutanga, izvi zvinongopesana zvishoma chete mukubatana pamwe nekufamba kwemaoko nemaoko. Izvi zvinogona kunge zvishoma kana zvishoma. Zvishoma nezvishoma, vanobata muviri wose uye vanogara vakanyarara, kudya kana kupfeka zvinenge zvisingaiti. Zvadaro, zvimwe zviratidzo zvehutano hwaHuntington dzinotanga kubatana nechiratidzo ichi:
- matambudziko nekutora nekucheka;
- kuipa kwekutaura;
- matambudziko nehope;
- kukanganisa kwematauriri toni.
Pakutanga kwekutanga, pangava nekusawirirana kwehutano hwemunhu uye kusangana kwemagariro. Semuenzaniso, murwere ane kuputsa kwemabasa ekufungidzira kusinganzwisisiki. Somugumisiro, haagoni kuronga zviito, kuzviita uye kuvapa kuongororwa kwakakwana. Zvadaro zvinetso zvinowedzera kuoma: munhu anova nehasha, kuita zvepabonde kuzvirambidza, kuzvidzora, pfungwa dzisingabatsiri dzinooneka uye kushaya zvinodhaka (kudhakwa, kubhejera) kunowedzera.
Kuongororwa kwezvirwere zveHuntington
Kuongororwa kwehutano hwaHuntington kunoitwa nenzira dzakasiyana-siyana dzekuongorora kwepfungwa uye kuongorora kwepanyama. Pakati penzira dzinobatsira, nzvimbo huru inobatwa nemaginiti resonance imaging uye computed tomography. Iko nekubatsira kwavo kuti iwe unogona kuona nzvimbo yeupfungwa hwehupi.
Kuongorora maitiro ekushandisa kunoshandiswa kubva pakuongorora maitiro. Kana zvinopfuura 38 trinucleotide zvakasara zveCAG zvinowanikwa muHD gene, chirwere chaHuntington chichapedzisira chichibuda mu100% emhosva. Muchiitiko ichi, zviduku nhamba yemasara, iyo gare gare muupenyu huchaonekwa icharatidzira chorea.
Kurapa kweHwere hwaHuntington
Nhamo, chirwere chaHuntington hachigoneki. Panguva ino, pakurwisana nechirwere ichi, chete chirwere chinoshandiswa chinoshandiswa chinoshandiswa, icho chinogadzirisa mamiriro ekurwara kwenguva pfupi.
Mushonga unobudirira kwazvo, unowedzera zviratidzo zvechirwere, ndiTetrabenazine. Uyewo mukurapa iyi inorwisa anti-Parkinsonian zvinodhaka:
- Bromocriptine;
- Levodopa;
- Pergolid.
Kuti abvise hyperkinesia uye kubvisa musimba kugadzikana, valproic acid inoshandiswa. Kurapa kwekuora mwoyo mune chirwere ichi kunoitwa naProzac, Citalopram, Zoloft uye mamwe anosarudza serotonin reuptake inhibitors. Apo painokura psychoses, atypical antipsychotics (Risperidone, Clozapine kana Amisulpride) inoshandiswa.
Upenyu huripo kuvanhu vanotambura nechirwere chaHuntington zvakanyanya kuderedzwa. Kubva panguva yekuonekwa kwekutanga zviratidzo zvehutano uku kusvika pakufa zvinogona kupfuura makore gumi nemashanu chete. Panguva imwecheteyo, inouraya
- kuzviuraya;
- pneumonia;
- pathology of the heart.
Nokuti ichi chirwere chechirwere, kudzivirira pachako hakupo. Asi kubva pakushandiswa kwekuongorora maitiro (kusarudzwa kwepabonde neDNA analysis) hazvidikanwe kuramba, nokuti kana pakutanga kwekutanga kutarisa zviratidzo, iwe unogona kuwedzera kwenguva refu hupenyu hwomurwere.