Gilbert syndrome - zvose zvinorwara zvehutano

Gilbert syndrome chirwere chinokonzerwa nemararamiro ane chiremera chinosanganiswa nemasabolism ye bilirubin . Somugumisiro, uwandu hwezvinhu zviri muropa hunowedzera, uye murwere pane imwe nguva ane chirwere chinonzi jaundice chakanaka - kureva kuti, ganda uye mucous rinova yerima. Panguva imwe chete, mamwe ose emiganho eropa uye kuedza kwechiropa zvinoramba zvakakwana.

Gilbert's syndrome - chii chiri mumashoko mashoma?

Chinonyanya kukonzera chirwere ichi ndiko kupererwa kwegene rinokonzera glucuronyl transferase, enzyme yepamusoro inokonzera kushandiswa kwebilirubin. Kana iyi enzyme mumuviri isingakwanisi, iyo chinhu haigoni kubudiswa zvachose, uye zvizhinji zvacho zvinopinda muropa. Apo kuiswa kwebilirubin kuwedzera, jaundice inotanga. Mune mamwe mazwi, kungotaura chete: Gilbert's disease ndiko kusakwanisa kwechiropa kukonzera dutu rine uturu mune zvakawanda zvakakwana uye kuchibvisa.

Gilbert's syndrome - zviratidzo

Chirwere ichi kazhinji kaviri katatu kakawanda kazhinji chinowanikwa mune varume. Sezvo mutemo, zviratidzo zvekutanga zvinowanikwa pazera remakore matatu kusvika ku13. Gilbert syndrome mwana anogona kuwana "nhaka" kubva kuvabereki. Mukuwedzera, chirwere ichi chinopesana nechekupedzisira kwekushaya nzara kwenguva refu, zvirwere, muviri uye kushungurudzika mupfungwa. Dzimwe nguva chirwere chinoonekwa nekuda kwekudya kwehomoni kana zvinhu zvakadai se caffeine, sodium salicylate, paracetamol.

Chiratidzo chechirwere chinonzi jaundice . Inogona kunge iri mukati-kati (kuonekwa mushure mekunwa doro, zvichiguma nekuda kwepanyama zvakanyanya kana kushungurudzika mupfungwa) uye kusingaperi. Mune vamwe varwere, uwandu hwebilirubin muGilbert's syndrome hunokwira zvishoma, uye ganda rinongowanikwa kanyoro kadiki, asi mune vamwe kunyange vatsvene vemaziso vanove vakajeka. Muzviitiko zvisingawanzoitiki, jaundice inenge yakasvibiswa.

Mukuwedzera kune ruvara rweganda uye mucous membrane, Gilbert's disease ine zviratidzo zvinotevera:

Gilbert's syndrome - kuongororwa

Kuti uone chirwere ichi, iwe unofanirwa kuitisa zvidzidzo zvekliniki dzinoverengeka panguva imwe chete. Inoda kuongororwa ropa kweZhibera syndrome. Mukuwedzera kwairi, murwere anopiwa:

Kuongorora kweGilbert's syndrome - kunyorwa

Migumisiro yeongororo yeongorori nguva dzose inonetsa kuparadzanisa. Kunyanya, apo paine vazhinji vavo, sekunyatsoongorora chirwere ichi. Kana pane kusafungirwa kweZibera syndrome, uye bilirubin mukutsvakurudza kunodarika mitemo ye 8.5 - 20.5 mmol / l, zvino kuongorora kunosimbiswa. Chiratidzo chisina kunaka ndehupo hwehutu hunopisa muhuini. Chinokosha - zviratidzo zvehutachiona hwehutachipatachi mune chirwere hazvigadziriswi.

Genetic kuongorora kweGilbert's syndrome

Nemhaka yokuti chirwere chacho chinowanzova nhaka, zvirwere zvinowanzoongorora zvinosanganisira DNA tsvakurudzo. Zvinotendwa kuti chirwere chacho chinoparidzirwa kumwana chete kana vabereki vose vari vatakuri vegomu risina kunaka. Kana mumwe wehama asingakwanisi, mwana achazvarwa akaine utano hwakanaka, asi panguva imwechete ichava mutakuri we "gadzirisa" jeni.

Sarudzai homozygous Gilbert chirwere muDNA kuongororwa kungave nokuongorora nhamba ye TA inodzokorora. Kana ivo vari munharaunda yekukurudzira yejeni 7 kana kupfuura, kuongorora kunosimbiswa. Nyanzvi dzinokurudzira zvakasimba kuitisa chirwere chemajini vasati vatanga kurapwa, kunyanya kana kurapwa nemishonga ine hepatotoxic zvinotarisirwa.

Nzira yekurapa sei Gilbert's syndrome?

Zvakakosha kunzwisisa kuti iyi haisi chirwere chinowanzoitika. Saka, mukurapa kwakakwana Gilbert's syndrome haifaniri. Vadzidza nezvekutsvaga kwavo, varwere vanokurudzirwa kuti vadzoke zvakare kudya - kuedza kuderedza kushandiswa kwemvura, yakanyanya, -kuedza kuzvizvidzivirira kubva pakunetseka uye mune ruzivo, kurega tsika dzakaipa, kana zvichibvira kurarama mararamiro akanaka. Kungotaura, hapana chakavanzika chekuporesa Gilbert's syndrome. Asi zviyero zvose zvinorondedzerwa pamusoro apa zvinogona kuita kuti uwandu hwebilirubin hudzoke zvakare.

Zvinodhaka neGilbert's syndrome

Sarudza mishonga chero ipi zvayo inofanira kuva nyanzvi. Semitemo, zvinodhaka neGilbert syndrome zvinoshandiswa zvakadai:

  1. Mishonga kubva kuboka rebarbiturate. Aya mishonga ine antiepileptic effect, pakufanana kufanana nehuwandu hwebilirubin.
  2. Hepatoprotectors . Chengetedza chiropa kubva pamigumisiro yakaipa yekushushikana.
  3. Muhupo hwehutachiona hwemawere, Gilbert's syndrome inorapwa ne antiemetics uye digestive enzymes.
  4. Inosorbents inobatsira kubviswa nokukurumidza kwebilirubin kubva mumukumbo.

Kudya muGiribert's syndrome

Muzvokwadi, chikafu chakakosha ndicho chinhu chinoita kuti kubudirira kwekudzorerwa kwechirongwa chinowanzoitwa bilirubin muropa. Kudya neGilbert's disease kunoda zvakasimba. Asi inoshanda. Varwere vane chirwere ichi vanobvumirwa kudya:

Uye zvakagadzirwa neGilbert's chirwere zvinorambidzwa sezvizvi:

Gilbert chirwere - kurapwa nemishonga yevanhu

Hazvibviri kuvimba chete pane dzimwe nzira dzokurapa. Asi chirwere chaAugustin Gilbert chimwe chezvirwere zvakadaro, umo chirwere chevanhu chinogamuchirwa kunyange nevanyanzvi vakawanda. Chinhu chikuru ndechekukurukura mishonga yemishonga kune chiremba anoenda, kunyatsotsanangurira muyero iwe pachako uye usakanganwa kugara uchitora matanho ose anodiwa ekudzivirira.

Gilbert syndrome - kurapwa kwamafuta newaini nehuchi

Zvisungo:

Kugadzirira, shandisa:

  1. Sakanidza zvose zvinoshandiswa zvakakwana mune imwe mudziyo uye udururire mugirazi, rakanyatsovharwa.
  2. Chengetedza mishonga munzvimbo inonaya yakasviba (pazasi pasi refriji, somuenzaniso).
  3. Usati washandisa, mvura inofanira kudziviswa nehuni yehuni.
  4. Inwa inenge 15 - 20 maminitsi makumi maviri nemakumi matatu mushure mekudya 3 kusvika ku5 pazuva.
  5. Jaundice inotanga kuburuka pazuva rechitatu, asi mishonga inofanira kudhakwa kwevhiki. Kuputsa pakati pemakato kunofanira kuva vhiki masere.

Kurapa kwaGilbert's syndrome ine burdock

Zvisungo:

Kugadzirira, shandisa:

  1. Zvinokurudzirwa kushandisa mashizha matsva akaunganidzwa muna May, kana aine huwandu hwakawanda hwezvinhu zvinobatsira.
  2. Pukuta magidhi nemvura.
  3. Juice inokurudzirwa kunwa 15 ml katatu pazuva kwemazuva gumi.

Chii chakaipa Gilbert syndrome?

Chirwere hachisi kutungamirira kurufu uye hupenyu hwehupenyu hahupfuuri. Asi mune izvi, Gilbert's syndrome ine migumisiro yakaipa mushure mezvose. Kwemakore, vamwe varwere vane jaundice vanogona kukura nekusawirirana kwepfungwa. Chii chingave chinonyanya kukanganisa nzira yekugadzirisa hutano hwevanhu uye hunoita kuti munhu aende kumuongorori wepfungwa.

Muzviitiko zvisingawanzoitiki, Gilbert syndrome inobvisa mabwe akavezwa mujecha kana mumatope echando. Kana izvi zvikaitika, saka nekuda kwekuwedzerwa kwezvakawandisa zvisinganzwisisiki bilirubin, kukonzera. Chiropa chinoshandiswa zvinenge zvisinei. Asi kana usingaregi kunwa doro, zvokudya zvinokuvadza uye kutora mishonga isingaregi, hepatitis inogona kukura.

Gilbert's syndrome uye pamuviri

Pakarepo zvakakosha kudzivisa vanaamai vari mberi: chirwere ichi uye pamuviri hazvibvumi. Gilbert's syndrome haigoni kutyisidzira mukadzi kana mwana wake weramangwana. Dambudziko guru rekuzivisa chirwere panguva inofadza mamiriro ezvinhu hazvibviri kutora mishonga iyo inowanzoshandiswa kugadzirisa mamiriro evarwere.

Gilbert syndrome inotora nhaka, asi amai vane ramangwana vanogona kuderedza kuwanda kwebilirubin muropa. Nekuda kwaunoda:

  1. Kunyatsopedza basa remuviri.
  2. Rega doro.
  3. Dzivisa kunyange kushungurudzika.
  4. Usava nenzara pane zvose.
  5. Gara muzuva kwechinguva chiduku.