Aplasia yeinso (Russell Silver Syndrome) ndeimwe yepenital anomalies yensoyo kukura. Iyo inoratidzirwa nekushaikwa kwakakwana kwechirongwa kana kusimba kwayo pasi. Izvi zvinogona kukanganisa kuonekwa kwe pyelonephritis, nephrolithiasis uye kuwedzera kwehutano.
Zviratidzo zvepori aplasia
Aplasia yeinso inowanikwa apo chinyorwa chemethanephros hachikure ku metanephrogenic blastema. Ikureter inogona kuva yezvakanaka uye shoma. Muzviitiko zvisingaiti, hazvisi zvachose. Chiratidzo chinowanzoitika cheplasia yehitsvo yakasara kana yakarurama inoderera muwandu wemuyo kana kusavapo. Uyewo, kusavapo kwechimwe chikamu chechiri ichi kunobvumira mumwe-rutivi rwechirume renal colic (uku ndiko kurwiswa kwemarwadzo anorwadza pamwe chete ne anuria). Hapana humwe zviratidzo muhutano huno.
Kuongororwa kwetsvo kupera
Kuti uongorore aplasia yemafungiro ari kuruboshwe kana kurudyi, zvakakosha kuita ultrasound kuongororwa kwemuviri wechipfu. Uyewo, kuvapo kwenhengo iri pasi pekushandiswa kana kusasipo kwayo kunogona kutsunga kushandisa:
- computed tomography with contrast;
- renal angiography;
- Excretory urography.
44.0-80.0 μmol / L ndiyo inowanzoita creatinine muropa remukadzi, asi neaplasia yeimpso iyi inogona kuderedzwa zvishoma. Saka, kana pane zviratidzo zvehutano hwakadaro, iwe unofanirwawo kutora ropa.
Kurapa kwepimpere aplasia
Aplasia yemafungiro akanaka kana kuruboshwe kazhinji haadi chirwere cherapi. Kuti uchengetedze hutano hwevanhu mune imwe nyika, iwe unongoda kutevera kudya kunenge kwakagadzirirwa kuderedza mutoro pamutsipa wechipiri. Kana murwere aine huwandu hwehutano hwepamusoro, zvino anofanira kutora diuretics.
Kupindira kwekuperesa nemaaplasia kwakashandiswa apo kana:
- kukura kwe hypertension (chete nephrogenic fomu);
- kuvapo kwekutambudzika kwakanyanya munzvimbo yakakanganiswa;
- reflux in the ureter, which malorazvit.