Antiphospholipid syndrome uye pamuviri

Antiphospholipid syndrome (APS) iboka rematambudziko anokonzerwa nemagadzirirwo ayo anozivikanwa nekuumbwa kwenhamba yakawanda yezvirwere kune phospholipid iri muropa reropa (antiphospholipid antibodies). Pakati pevakadzi vanotambura nokupererwa , huwandu hwe antiphospholipid syndrome hwakakwirira, uye hunobata 28-43%. Icho chinetso chikuru chechipatara ichi ndecheprombosi.

Ndezvipi zvikonzero zvikuru zvekusimudzirwa kweAAPS?

Zvinokonzera kukura kwe antiphospholipid syndrome zvishoma. Izvi zvirwere zvinogona kukura mumatambudziko anotevera:

  1. Apo mukadzi ari kurwara ne systemic lupus erythematosus .
  2. Kuvapo mu anamnesis we thrombosis. Kana midziyo yakakanganiswa iyo inopa ropa kumutsipa, iyo inonzi "mudumbu rembodhi" inokura, iyo inoratidzika nechitarisiko chekusimudzira, kuvhara marwadzo mukati mechidziro chemuviri pakarepo mushure mekudya.
  3. Kuderedza kweplatelets muropa, iyo isingafambidzwi nehutachiona hunoitika.
  4. Kuvapo kwenhau ye myocardial infarction nedzimwe zvirwere zvinosangana nemararamiro emwoyo ekuzungunusa.

Ko antiphospholipid syndrome inoratidzika sei?

Symptoms of antiphospholipid syndrome, zvakananga zvichienderana nezvimwe zvinhu. Saka zvakakosha ndezvizvi zvinotevera:

Saka, munyaya iyo pane kuvharwa kwemidziyo miduku, kutyora kwakanyanya kwemabasa echikwata chinopihwa kunochengetwa. Semuenzaniso, kana hutachiona hwemadiki vascular reticulums hunovhiringidzika, kune kukanganisa kwechibvumirano chezvikamu zvemuyocardium, asi kana chiedza chekoniyoni ichivharwa, myocardial infarction ichaitika.

Kazhinji antipospholipid syndrome muvakadzi vane pamuviri vanogona kutevedzera zvimwe zvirwere zvakasiyana-siyana, izvo zvinoratidzwa nezviratidzo zvakafanana. Nokudaro, zviratidzo zve antiphospholipid syndrome zvinogona kuratidzirwa muhupo hwertico lyvedo (lacy, mesh mhete yemidziyo iri paganda). Uyewo, zvirwere zvisingaperi zvechirwere, izvo zvakaoma kurapa, uye kunyange mhirizhonga inoputika, inogona kuratidza kuvapo kwehutano huri mumuviri.

Kurapa kunoitwa sei?

Kurapa kwe antiphospholipid syndrome pakuberekwa kunoitwa pasi pesimba rechiremba vaviri: gynecologist uye rheumatologist. Chirwere chekutanga chechirwere ichi ndechokushandisa glucocorticoids uye cytostatics. Nehupamhi hwehutachiona huri muropa, mhinduro chete ndiyo yekuita plasmapheresis (kuchenesa ropa).